Childhood macular dystrophies
There are two types of macular retinal dystrophy. A form called Best disease usually appears in childhood and causes different amounts of vision loss. The second usually affects you in midadulthood. It causes vision loss that slowly gets worse. People with Best disease usually have a parent who has it.Macular dystrophies are a large number of rare, inherited conditions that affect central vision. They can appear in childhood, but some are not diagnosed until later in life. childhood macular dystrophies
Introduction. Hereditary dystrophies affecting the central retina in children and adolescents represent a heterogeneous group of diseases. Genetic alterations may be responsible for changes of the choroid (choroideremia), of the retinal pigment epithelium [RPE (Best's disease), of the photoreceptor outer segments (Stargardt's disease),
Oct 23, 2002 Macular dystrophy is a condition which appears earlier in life, and causes a reduction in central vision found in the macula, the central portion of the retina. Macular dystrophies are usually inherited in a predictable pattern within families. How can the answer be improved?childhood macular dystrophies Childhood Retinal Dystrophies The retina is a light sensitive tissue layer lining the inner back surface of the eye. The function of the retina is to change light signals coming into the eye into an image in the form of electrical signals.